Long QT syndrome (LQTS) is a cardiac disorder associated with sudden death especially in
young, seemingly healthy individuals. It is characterised by abnormalities of the heart beat
detected as lengthening of the QT interval during cardiac repolarisation. The incidence of
LQTS is given as 1 in 2000 but this may be an underestimation as many cases go
undiagnosed, due to the rarity of the condition and the wide spectrum of symptoms.
Presently 12 genes associated with LQTS have been identified with differing signs and …